Posterior fossa haemangioblastoma
35 years female with progressive headache and ataxia.
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Well defined cystic mass measuring 4.43 x 3.71 cm involving the left cerebellum and showing mild perilesional oedema and mass effect with compression of the fourth ventricle causing hydrocephalus.
There is an eccentric strongly enhancing nodule lesion abutting the lateral wall of the cyst.
There are prominent vessels overlying the nodule.
No calcification or haemorrhage
MRI shows typical features of posterior fossa hemangioblastoma. Waiting for histological confirmation.
Haemangioblastomas are vascular origin tumours in patients with von-Hippel Lindau (vHL) disease.
87-97% are intracranial, 55% in the posterior fossa, and 85% in the cerebellar hemisphere
Haemangioblastomas are rare under 15 years, with a peak age between 30-65 years; similar lesions in the posterior fossa among children are pilocytic astrocytomas.