Posterior fossa haemangioblastoma

Case contributed by Dr Subash Thapa

Presentation

35 years female with progressive headache and ataxia.

Patient Data

Age: 35-year-old
Gender: Female
MRI

MRI Brain

Well defined cystic mass measuring 4.43 x 3.71 cm involving the left cerebellum and showing mild perilesional oedema and mass effect with compression of the fourth ventricle causing hydrocephalus.

There is an eccentric strongly enhancing nodule lesion abutting the lateral wall of the cyst.

There are prominent vessels overlying the nodule.

No calcification or haemorrhage

Case Discussion

MRI shows typical features of posterior fossa hemangioblastoma. Waiting for histological confirmation. 

Haemangioblastomas are vascular origin tumours in patients with von-Hippel Lindau (vHL) disease. 

87-97% are intracranial, 55% in the posterior fossa, and 85% in the cerebellar hemisphere

Haemangioblastomas are rare under 15 years, with a peak age between 30-65 years; similar lesions in the posterior fossa among children are pilocytic astrocytomas

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Case information

rID: 40570
Case created: 26th Oct 2015
Last edited: 17th Jan 2016
Inclusion in quiz mode: Included

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