Posterior fossa hemangioblastoma
35 years female with progressive headache and ataxia.
Loading Stack -
0 images remaining
Well defined cystic mass measuring 4.43 x 3.71 cm involving the left cerebellum and showing mild perilesional edema and mass effect with compression of the fourth ventricle causing hydrocephalus.
There is an eccentric strongly enhancing nodule lesion abutting the lateral wall of the cyst.
There are prominent vessels overlying the nodule.
No calcification or hemorrhage
MRI shows typical features of posterior fossa hemangioblastoma. Waiting for histological confirmation.
Hemangioblastomas are vascular origin tumors in patients with von-Hippel Lindau (vHL) disease.
87-97% are intracranial, 55% in the posterior fossa, and 85% in the cerebellar hemisphere
Hemangioblastomas are rare under 15 years, with a peak age between 30-65 years; similar lesions in the posterior fossa among children are pilocytic astrocytomas.