Primary sclerosing cholangitis

Case contributed by Henry Knipe
Diagnosis almost certain

Presentation

Abnormal LFTs.

Patient Data

Age: 20 years
Gender: Female

Generalized intrahepatic biliary dilatation with multifocal biliary stricturing leading to a "beading appearance". 

Case Discussion

This is a known case of primary sclerosing cholangitis in a young patient with ulcerative colitis.

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