Primary sclerosing cholangitis

Case contributed by Dr Jan Frank Gerstenmaier

Presentation

This patient with known Crohn disease presented with abnormal liver enzymes.

Patient Data

Age: 55
Gender: Male
MRI

MRCP

There is atrophy of the right lobe of the liver. The intrahepatic biliary tree demonstrates multifocal stricturing and beading. There is a short stricture just central to the confluence with a short segment of mild duct dilatation at 7mm with a normal calibre CBD distally at 4mm. The pancreatic duct is normal. Appearances are in keeping with early PSC.

 

Case Discussion

The association between primary sclerosing cholangitis and inflammatory bowel disease is strong (in 70% of cases), as in this patient. Caudate hypertrophy is often seen in advanced disease (not present here). The most feared complication is cholangiocarcinoma which develops in up to 15% of patients.,

PlayAdd to Share

Case information

rID: 30910
Case created: 9th Sep 2014
Last edited: 9th Jan 2016
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.