Primitive neuroectodermal tumour of the CNS

Case contributed by Dr Bruno Di Muzio

Presentation

Young child with a supratentorial mass.

Patient Data

Gender: Male

CT Brain

Modality: CT

CT demonstrates a very large right hemispheric mass, which is markedly heterogeneous in attenuation, with both cystic and hyperdense components; the latter representing hemorrhagic components (see MRI). Following administration of contrast, the mass enhances heterogeneously. Large feeding vessels can be appreciated, including (within the limitations of a non-CTA study) external carotid artery (both superficial temporal artery branches which pass through the thinned parietal bone, and middle meningeal which is markedly enlarged) and middle cerebral artery

MRI Brain (selected images)

Modality: MRI

MRI confirms the presence of haemorrhagic components as areas of signal drop out on T2* weighted sequence.

Case Discussion

CT demonstrates a very large right hemispheric mass, which is markedly heterogeneous in attenuation, with both cystic and hyperdense components; the latter representing hemorrhagic components (see MRI). Following administration of contrast, the mass enhances heterogeneously. Large feeding vessels can be appreciated, including (within the limitations of a non-CTA study) external carotid artery (both superficial temporal artery branches which pass through the thinned parietal bone, and middle meningeal which is markedly enlarged) and middle cerebral artery

MRI confirms the presence of haemorrhagic components as areas of signal drop out on T2* weighted sequence.

Given the supratentorial location and large size and heterogeneous appearance, in a young child the favored diagnosis is a primitive neuroectodermal tumour of the CNS.

Histology was told to confirms the diagnosis of primitive neuroectodermal tumour of the CNS.

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Case Information

rID: 12558
Case created: 16th Dec 2010
Last edited: 4th Sep 2015
Inclusion in quiz mode: Included

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