Prune belly syndrome

Case contributed by Dr Aditya Shetty

Presentation

Antenally diagnosed on ultrasound with hydronephrosis (bilateral), hydroureter and large bladder.

Patient Data

Age: neonate
Gender: Male
X-ray

X ray findings:

  • globular shape of abdomen
  • bilateral bulging flanks

Prune belly syndrome can be diagnosed by an antenatal ultrasound.

  • abnormal large abdominal cavity
  • hydroureteronephrosis and large distended bladder 
  • the abdomen swells with the pressure of accumulated urine and
  • no resistance offered to swelling due to lack of abdominal muscles

Triad of Prune belly syndrome:

  • urinary tract abnormalities i.e. bilateral hydroureteronephrosis 
  • anterior abdominal wall musculature is underdeveloped  or absent
  • Bilateral undescended testes (cryptorchidism)

Case Discussion

Case of Prune belly syndrome

  • also known as the Eagle Barrett syndrome  or the triad syndrome.

  • this case shows an X-ray of a still born child

  • the gross bilateral hydronephrosis coupled with absence of abdominal musculature has caused bulging of the flanks
  • the child was still born probably due to complication of pulmonary hypoplasia
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Case information

rID: 28224
Case created: 16th Mar 2014
Last edited: 12th Nov 2017
System: Paediatrics
Tag: shetty
Inclusion in quiz mode: Included

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