Prune belly syndrome

Case contributed by Dr Hidayatullah Hamidi

Presentation

Irritability, poor urination.

Patient Data

Age: Neonate
Gender: Male
Photo

Anterior abdominal wall underdevelopment resulting in the "prune belly" appearance.

Ultrasound

Bilateral hydroureteronephrosis is noted.

Both testes were not present in the scrotal cavities.

CT

Bilateral moderate to severe hydroureteronephrosis is seen with tortuous dilated ureters. Persistent renal fetal lobulation is seen.

Urinary bladder shows thickened walls.

Underdeveloped abdominal wall.

Case Discussion

The case comprises all three major findings of Prune belly syndrome (also known as Eagle Barrett syndrome or triad syndrome)

  1. gross pelvicalyceal and ureteric dilatation with renal dysplasia
  2. anterior abdominal wall underdevelopment (resulting in the "prune belly" appearance)
  3. bilateral undescended testes (cryptorchidism)

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.