Presentation
Irritability, poor urination.
Patient Data
Age: Neonate
Gender: Male
From the case:
Prune belly syndrome
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Anterior abdominal wall underdevelopment resulting in the "prune belly" appearance.
From the case:
Prune belly syndrome
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Bilateral hydroureteronephrosis is noted.
Both testes were not present in the scrotal cavities.
From the case:
Prune belly syndrome
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Bilateral moderate to severe hydroureteronephrosis is seen with tortuous dilated ureters. Persistent renal fetal lobulation is seen.
Urinary bladder shows thickened walls.
Underdeveloped abdominal wall.
Case Discussion
The case comprises all three major findings of Prune belly syndrome (also known as Eagle Barrett syndrome or triad syndrome)
- gross pelvicalyceal and ureteric dilatation with renal dysplasia
- anterior abdominal wall underdevelopment (resulting in the "prune belly" appearance)
- bilateral undescended testes (cryptorchidism)