Pseudocoarctation of the aorta

Case contributed by Jose Ignacio Aragon

Presentation

Asymptomatic, suspicion of thoracic aorta aneurysm.

Patient Data

Age: 50 years
Gender: Male

CTA of the aorta

ct

Buckling of the thoracic aorta at the level of the ligamentum arteriosum with elongation of the descending portion, without focal stenosis or marked dilation. No collateral vessel formation. 

Case Discussion

This is a rare anomaly characterized by a buckling or kinking of the descending aorta at the level of the ligamentum arteriosum, without significant hemodynamic obstruction or pressure gradient across the lesion, and therefore no collateral vessel formation.

Embryologic theory: failure of compression and fusion of the third through tenth segments of the dorsal aortic roots and of the left fourth arch segment when the cephalic shift of the seventh dorsal intersegmental artery occurs. As a result, the aortic arch is longer than normal, and eventually twists or kinks at the point of insertion of the ligamentum arteriosum. Pseudocoarctation may also result from a short, taut ligamentum arteriosum or PDA. 

This entity is usually asymptomatic and does not need interventional treatment in most of the cases. 

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.