Presentation
Right heart failure for transplant assessment
Patient Data
Age: 70 years
Gender: Female
From the case:
Pulmonary agenesis
Frontal
Small relatively opaque left hemithorax with mediastinal shift and elevated hemidiaphragm.
Large proximal right pulmonary arteries.
Scoliosis.
From the case:
Pulmonary agenesis
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Axial C+ arterial phase
Single right lung herniating across the midline.
No left bronchus or pulmonary artery.
Pulmonary hypertension due to large secundum ASD: RV dilated and hypertrophied.
Case Discussion
The absence of left bronchial stub distinguishes agenesis from hypoplasia.
ASD and scoliosis are features of VACTERL.