Pulmonary artery aneurysms

Case contributed by Dr Ahmed Abd Rabou

Presentation

Known case of "a systemic disease", develops chest pain and dyspnea.

Patient Data

Age: 35 years old
Gender: Male
Modality: CT

A saccular aneurysm arises from the descending branch of each pulmonary. Another large aneurysmal sac with large mural thrombus is seen at the left lingular region likely arising from segmental branch. Nevertheless, there is thrombosed SVC with development of collateral pathways through the prominent azygos/hemiazygos as well as IVC-hepatic veins-internal mammary veins pathoway.

Case Discussion

Behcet disease is a sort of systemic vasculitis characterized by oral and genital ulcers as well as uveitis of the eye. Thoracic manifestations of Behcet disease include multiple bilateral pulmonary artery aneurysms that are of fusiform or saccular type and usually involves the main pulmonary artery or its descending branch. SVC obstruction developed secondary to inflammation of the vessel wall that led to thrombosis. Collateral pathways developed to bypass the thrombosed SVC.

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Case Information

rID: 32749
Case created: 11th Dec 2014
Last edited: 6th Dec 2016
System: Chest
Inclusion in quiz mode: Included

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