Pulmonary atresia with intact interventricular septum

Case contributed by Dr Henry Knipe

Presentation

NICU admission x-ray.

Patient Data

Age: 3 days
Gender: Female

Marked enlargement of the cardiac silhouette. No pulmonary plethora. No focal consolidation, collapse or pleural effusion. Nasogastric tube tip projects in the region of the gastro-esophageal junction. 

Case Discussion

These findings are non-specific for the particular type of congenital heart disease. Echocardiography demonstrated pulmonary atresia with intact interventricular septum as the underlying cause for cardiomegaly. Not in this case but there is sometimes pulmonary plethora

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