Retinal detachment due to diffuse choroidal hemangioma in a case of Sturge-Weber syndrome
Presentation
Seizures and facial port-wine stain on the right side of the face
Patient Data
Right-sided parietotemporal lobar volume loss with subcortical white matter T2GRE hypointense lesions due to calcifications. Mild enlargement of the right choroid plexus is also noted.
In the ipsilateral orbit, diffuse choroidal thickening with FLAIR hyperintense signal is present.
Findings are compatible with Sturge-Weber syndrome with possibly diffuse choroidal hemangioma in the right globe.
8 months later
After 8 months the same patient presented with acute progressive reduced visual acuity.
MR demonstrates exudative retinal detachment on the right side with subretinal hemorrhage, which hyperintense on T1WI. There is homogeneously enhancing diffuse lentiform choroidal lesion on the posterior aspect of the right globe, most keeping with diffuse choroidal hemangioma. There is also right-sided prominent leptomeningeal enhancement due to pial angiomatosis.
Case Discussion
Choroidal hemangiomas are benign hamartomas os the choroid. The diffuse form usually associates with Sturge-Weber syndrome. Choroidal hemangiomas can complicate with retinal detachment and subretinal hemorrhage.