Retroperitoneal lymphangiectasia and transposition of inferior vena cava

Case contributed by Mohamed Saber
Diagnosis almost certain

Presentation

Abdominal pain mainly epigastric.

Patient Data

Age: 30 years
Gender: Male

There are pelviabdominal bilateral retroperitoneal prominent serpiginous structures of low density suggestive of retroperitoneal lymphangiectasia. Associated mild dilatation of the cisterna chyli and thoracic duct is also noted.

Left-sided inferior vena cava terminates at the level of the left renal vein and crosses anterior to the aorta to join the normal pre-hepatic segment of IVC. The right renal vein normally drains to the IVC. A venous structure is seen to the right of the aorta communicates the IVC at the level of the right renal vein to the right common iliac vein probably a variant of IVC duplication. 

Case Discussion

Here is a case of retroperitoneal lymphangiectasia, which is usually due to a congenital developmental anomaly of the lymphatic vessels however it could be also secondary to infections like filariasis, malignancies, or post-operative and radiation therapy. In our case, it is incidentally discovered, with no known underlying cause likely congenital. Its relation to the patient's complaint is controversial.

Another finding is the transposition of inferior vena cava with a probable variant of IVC duplication.

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