Presentation
Known case of neurofibromatosis. Presented with low backache since few months.
Patient Data
Age: 60 years
Gender: Male
From the case:
Sacral chordoma
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Sagittal T2
Large heterogenously enhancing lesion noted in the sacral region causing erosion and infiltration of the sacrum and posterior paraspinal muscles.
Case Discussion
This is a pathologically proven case of sacral chordoma.
However, in view of the history, imaging wise, malignant peripheral nerve sheath tumor could not be ruled out.
Sacral chordoma is the most common primary malignant sacral neoplasm. The tumor arises from intraosseous notochordal remnants.
Intraosseous peripheral nerve sheath tumors (PNSTs) are rare. Most of the intrasosseous PNST arise from head and neck due to the presence of intraosseous nerves in neuroforamina of head and neck.