Schizencephaly

Case contributed by Dr Roberto Schubert

Presentation

Grand mal seizures, right spastic hemiparesis.

Patient Data

Age: 35
Gender: Female
Modality: MRI

Left frontoparietal parenchymal cleft lined by grey matter and extending from the cortical surface to the lateral ventricle. The latter shows enlargement, a small ependymal defect at its lateral border and a large defect of the septum pellucidum. The corpus callosum is intact. There are severeal areas of polymicrogyria, not only at the borders of the defect but also at the superior left frontal lobe surface. Hetereotopic islands of grey matter can be found as well (supero-lateral to left ventricle). Also note the marked atrophy of the left cortico-spinal tract.

Case Discussion

Part of the walls of the defect are apposed against each other, but there is a small open portion above the Sylvian fissure that is continuous with the ventricles. Hence, it is not purely closed lip.

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Case Information

rID: 29672
Case created: 12th Jun 2014
Last edited: 9th Oct 2015
Inclusion in quiz mode: Included

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