Pre operative CXR.
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Heart size is within normal limits. Hypoplastic right lung with linear opacity consistent with venous drainage at the right lung base in keeping with known scimitar syndrome. The left lung is clear. No acute osseous abnormality.
Scimitar syndrome, also known as pulmonary venolobar syndrome or hypogenetic lung syndrome, is characterised by a hypoplastic lung that is drained by an anomalous vein into the systemic venous system. It is a type of partial anomalous pulmonary venous return.
Haemodynamically, there is an acyanotic left to right shunt. The anomalous vein usually drains into:
- inferior vena cava: most common
- right atrium
- portal vein