Presentation
Shortness of breath.
Patient Data
Age: 2 days
Gender: Male
From the case:
Scimitar syndrome
Frontal
Mediastinal shift to the right with near white-out of the right hemithorax.
From the case:
Scimitar syndrome
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Axial lung window
Hypoplastic right lung with mediastinal shift to the right and basal opacity. There is an anomalous pulmonary vein draining to the inferior vena cava. Systemic arterial supply to the right lower lobe is also demonstrated.
ETT tip is well above the carina. Mild cardiomegaly. No pleural or pericardial effusion. Hypoplastic right pulmonary artery.
Case Discussion
Scimitar syndrome (a.k.a. pulmonary venolobar syndrome or hypogenetic lung syndrome) is characterized by pulmonary hypoplasia that is drained by an anomalous vein into the systemic venous system. There is an uncommon association with lung sequestration (~10%).
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