Presentation
Right sided chest pain. Incidental finding.
Patient Data
Right well-defined supradiaphragmatic hypoattenuating non-enhancing 'pseudomass' measuring about 6 x 4 x 4 cm with abnormal aberrant small arterial supply from the abdominal aorta.
The right lung volume is reduced (hypoplastic).
The venous drainage is via the dilated single right pulmonary vein into the left atrium. The right-sided anomalous pulmonary vein drains into the IVC as part of the PAPVR,
Bilateral left-sided branching of the bronchial tree.
Case Discussion
This is a classic case of scimitar syndrome (hypogenetic lung syndrome), which is a combination of:
partial anomalous pulmonary venous return (PAPVR) in the right lower lobe with a dilated tortuous vein draining into the left atrium
hypoplastic right lung with a small feeding artery from the abdominal aorta
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