Scimitar syndrome

Case contributed by Dr Elias Bajotto Adaime

Presentation

New onset atrial fibrillation

Patient Data

Age: 30 years
Gender: Male
X-ray

Frontal chest x-ray shows mild volumetric reduction of right lung, in association with dextrocardia and a tubular shaped opacity along right cardiac border.

Oblique incidence displayed that tubular opacity as a venous structure, arising from the right hilum, extending to the inferior vena cava topography. These findings are highly suggestive of Scimitar syndrome, a form of partial pulmonary anomalous venous return (PAPVC).

CT

CT a confirmed the chest x-ray findings, along with right diaphragmatic herniation and some areas of reduced lung parenchymal attenuation, probably due to vascular perfusion disturbance.

Case Discussion

Scimitar syndrome is characterised by a hypoplastic lung that is drained by an anomalous vein into the systemic venous system.

PlayAdd to Share

Case information

rID: 56935
Published: 29th Nov 2017
Last edited: 16th Jul 2018
System: Cardiac, Chest
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.