Scimitar syndrome

Case contributed by Dr Elias Bajotto Adaime

Presentation

New onset atrial fibrillation

Patient Data

Age: 30 years
Gender: Male
X-ray

Frontal chest x-ray shows mild volumetric reduction of right lung, in association with dextrocardia and a tubular shaped opacity along right cardiac border.

Oblique incidence displayed that tubular opacity as a venous structure, arising from the right hilum, extending to the inferior vena cava topography. These findings are highly suggestive of Scimitar syndrome, a form of partial pulmonary anomalous venous return (PAPVC).

CT

CT a confirmed the chest x-ray findings, along with right diaphragmatic herniation and some areas of reduced lung parenchymal attenuation, probably due to vascular perfusion disturbance.

Case Discussion

Scimitar syndrome is characterized by a hypoplastic lung that is drained by an anomalous vein into the systemic venous system.

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Case information

rID: 56935
Published: 29th Nov 2017
Last edited: 18th Mar 2020
System: Cardiac, Chest
Inclusion in quiz mode: Included

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