Scimitar syndrome

Case contributed by Assoc Prof Craig Hacking


12 months of mild SOBOE.

Patient Data

Age: 25 years
Gender: Female

Curvilinear tubular opacity in the medial right lower zone paralleling the right heart border representing a scimitar. The right lung is slightly more dense and smaller than the left lung with decreased intercostal spacing. No pleural effusion. Heart size is normal.

Annotated image

Scimitar sword.

Case Discussion

This patient was subsequently referred externally for CTA which confirmed an anomalous right lower pulmonary vein draining into the IVC, in keeping with PAPVR.

Scimitar syndrome represents a combination of pulmonary hypoplasia and partial anomalous pulmonary venous return (PAPVR).

It almost exclusively occurs on the right side and the anomalous pulmonary vein can drain into the:

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