Presentation
12 months of mild SOBOE.
Patient Data
Age: 25 years
Gender: Female
From the case:
Scimitar syndrome
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Curvilinear tubular opacity in the medial right lower zone paralleling the right heart border representing a scimitar. The right lung is slightly more dense and smaller than the left lung with decreased intercostal spacing. No pleural effusion. Heart size is normal.
From the case:
Scimitar syndrome
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Scimitar sword.
Case Discussion
This patient was subsequently referred externally for CTA which confirmed an anomalous right lower pulmonary vein draining into the IVC, in keeping with PAPVR.
Scimitar syndrome represents a combination of pulmonary hypoplasia and partial anomalous pulmonary venous return (PAPVR).
It almost exclusively occurs on the right side and the anomalous pulmonary vein can drain into the:
- inferior vena cava: most common
- right atrium
- portal vein
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