Scimitar syndrome

Case contributed by Assoc Prof Craig Hacking

Presentation

12 months of mild SOBOE.

Patient Data

Age: 25 years
Gender: Female
X-ray

Curvilinear tubular opacity in the medial right lower zone paralleling the right heart border representing a scimitar. The right lung is slightly more dense and smaller than the left lung with decreased intercostal spacing. No pleural effusion. Heart size is normal.

Annotated image

Scimitar sword.

Case Discussion

This patient was subsequently referred externally for CTA which confirmed an anomalous right lower pulmonary vein draining into the IVC, in keeping with PAPVR.

Scimitar syndrome represents a combination of pulmonary hypoplasia and partial anomalous pulmonary venous return (PAPVR).

It almost exclusively occurs on the right side and the anomalous pulmonary vein can drain into the:

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Case information

rID: 73309
Published: 6th Jan 2020
Last edited: 14th Jun 2020
Inclusion in quiz mode: Included

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