Presentation
Shortness of breath.
Patient Data
Age: 30 years
Gender: Female
From the case:
Scimitar syndrome
Show annotations
Download
Info
Right-sided scimitar vein. Lungs clear, no pleural effusion, cardiac silhouette mildly enlarged. Slightly hypoplastic right lung.
From the case:
Scimitar syndrome
Show annotations
Download
Info
The right upper lobe drains into the left atrium, but the right middle and lower lobes drain into a large scimitar vein that in turn drains into the IVC at the level of the right hemidiaphragm. The right ventricle is enlarged.
Case Discussion
Scimitar syndrome is an uncommon combination of 2 congenital anomalies: 1) hypoplastic lung and 2) partial anomalous pulmonary venous return. The syndrome is almost always right-sided.
Unable to process the form. Check for errors and try again.