Scimitar syndrome (CMR)

Case contributed by David Cuevas


Exertional dyspnea.

Patient Data

Age: 45 years
Gender: Female

Cardiomegaly, likely due to right chambers enlargment. 

Tubular opacity in the lower lobe of the right lung.


Mild decrease in right lung volume with mild shift of the heart to the right. 

Enlargement of right cardiac chambers is confirmed.

Cine images demonstrating the main scimitar vein draining into inferior vena cava


Scimitar vein draining into inferior vena cava

Mild shift of the heart to the midline due to hypoplasic lung.

CT contributed by Dr Lazaro Delgado

Case Discussion

Classic example of Scimitar syndrome. Cine images accurately illustrate the connection of the scimitar vein.

Patients can be asymptomatic when <50% of the pulmonary circulation or remain subclinical, such as this case.

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