Presentation
Bilateral hand and wrist pain. Epigastric pain. Known case of scleroderma.
Patient Data
Age: 20 years
Gender: Female
From the case:
Scleroderma
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Bilateral tuft resorption is associated with fingertip soft tissue atrophy and peri-articular osteopenia. No abnormal soft tissue calcification.
Case Discussion
Scleroderma is an autoimmune disease characterized by multisystem fibrosis and soft tissue calcification.
The hands are the most common site of musculoskeletal involvement and characterized by:
- acro-osteolysis (resorption of distal phalanx)
- periarticular osteopenia
- joint space narrowing
- bony erosions
- subcutaneous and periarticular calcification
- atrophy of the fingertips
- hand deformity (flexion contractions)