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Scleroderma with interstitial fibrosis

Case contributed by Natalie Yang
Diagnosis almost certain

Presentation

Shortness of breath.

Patient Data

Age: Adult
Gender: Female

There are characteristic changes of pulmonary fibrosis, particularly in the bases and in the subpleural lung. Honeycomb change, intralobular septal thickening and traction bronchiectasis are all present. No pleural effusion or obvious nodal enlargement is visible.

The esophagus is dilated and air filled.

Case Discussion

The combination of basal pulmonary fibrosis and a dilated esophagus, is certainly suggestive of scleroderma.  Although not pathognomonic it should be considered highly likely, especially in a woman. 

In this case, the patient had clinically established scleroderma.

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