Scleroderma with interstitial fibrosis

Case contributed by Dr Natalie Yang

Presentation

Shortness of breath.

Patient Data

Age: Adult
Gender: Female

HRCT

Modality: CT

HRCT of the chest demonstrates characteristic changes of pulmonary fibrosis, particularly in the bases and in the subpleural lung. Honeycomb change, intralobular septal thickening and traction bronchiectasis are all present. No pleural effusion or obvious nodal enlargement is visible.

The oesophagus is dilated and air filled.

Case Discussion

The combination of basal pulmonary fibrosis and a dilated oesophagus, is certainly suggestive of scleroderma.  Although not pathognomonic it should be considered highly likely, especially in a woman. 

In this case, the patient had clinically established scleroderma.

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Case Information

rID: 8604
Case created: 16th Feb 2010
Last edited: 20th Mar 2017
System: Chest
Inclusion in quiz mode: Included

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