Scleroderma: with UIP type pulmonary fibrosis

Case contributed by Dr Abdallah Al Khateeb


Long standing GERD and dry cough.

Patient Data

Age: 40 years old
Gender: Female

Inter-lobular septal thickening and subpelural lines peripherally and basally, bilateral and symmetrical. Evidence of traction bronchietctesis and small air cysts. No frank evidence of honey-combing. No pleural effusion. 

A dilated patuolous esophagus with food material within.

Case Discussion

Scleroderma is a systemic disease with typical pulmonary involvement in the form of usual interstitial pneumonitis that, with time, progresses to fibrosis.

The presence of a dilated malfunctioning esophagus as in this case hints to the diagnosis, as it implies a systemic disease rather than an isolated pulmonary process.

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Case information

rID: 43592
Published: 20th Apr 2016
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

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