Presentation
No clinical information provided. Patient referred for aortic coarctation.
Patient Data
Age: 25 years
Gender: Male
From the case:
Shone complex
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Chordae tendineae attached mainly to a single papillary muscle (parachute mitral valve).
Thin mitral membrane
Left ventricular outflow tract partially obstructed by the ventricular septum; notice the flow artifact -occurs at a valvular level due to a bicuspid aortic valve. Severe ductal aortic coarctation associated with dilated mammary artery and scapular collaterals.
From the case:
Shone complex
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- blue arrowheads and arrow: chordae tendineae attached mainly to a single papillary muscle (parachute mitral valve)
- green arrowhead: thin mitral membrane
Case Discussion
Shone syndrome is a sporadic congenital heart disease involving four congenital left-sided cardiac anomalies:
- coarctation of the aorta
- mitral parachute valve
- supravalvular mitral ring
- subaortic stenosis