Shone complex

Case contributed by Dr David Cuevas

Presentation

No clinical information provided. Patient referred for aortic coarctation.

Patient Data

Age: 25 years
Gender: Male
mri

Chordae tendineae attached mainly to a single papillary muscle (parachute mitral valve).
Thin mitral membrane

Left ventricular outflow tract partially obstructed by the ventricular septum; notice the flow artifact -occurs at a valvular level due to a bicuspid aortic valve. Severe ductal aortic coarctation associated with dilated mammary artery and scapular collaterals.

Annotated image
  • blue arrowheads and arrow: chordae tendineae attached mainly to a single papillary muscle (parachute mitral valve)
  • green arrowhead: thin mitral membrane

Case Discussion

Shone syndrome is a sporadic congenital heart disease involving four congenital left-sided cardiac anomalies:

  • coarctation of the aorta
  • mitral parachute valve
  • supravalvular mitral ring
  • subaortic stenosis

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