Situs ambiguous, asplenia syndrome with bilateral right sidedness
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Archived case, no previous investigations were available.
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Dextro-position of the heart, absent spleen, transverse liver, bilateral trilobed lungs.
Incidental finding is the presence of two renal arteries are seen on each side.
Heterotaxy syndrome is the presence of certain organs forming on the opposite side of the body. It may affect the heart, liver, lungs, intestines, and spleen, yet the first identification in babies with heterotaxy syndrome is usually by problems with their hearts or livers.
It has no sex predilection and the heart is involved about 80% of cases. The etiology is not yet known. Few cases were reported to have some familial linkage.
Findings may include (all imaging findings need not be present):
- Thoracic: bilateral right sidedness, dextro- meso- or levocardia, bilateral SVC, absent coronary sinus and multiple associated congenital heart diseases.
- Abdominal: transverse liver, splenic agenesis, left sided stomach (with dextrocardia), right sided stomach (with levocardia) or midline stomach.
- 1. www.heterotaxy.org
- 2. Suhny Abbara. Diagnostic Imaging. (2013) ISBN: 9781931884747
22 public playlist include this case
- Cases RF by Dr Nikhil Rao
- ped by enasdonia enasdonia
- PAEDS by Gregory Makris
- Paeds assorted by Dr Arthur Daire
- svc by michele knox
- Abdo Cases by Ashlee Kates-Ascioti
- Paed - Chest - Clinical Conditions by Dr Charlie Handley
- Good cases by Jheyson Javier Barrios Pereira
- kinder by Ulrike Bartosch
- Pediatric Abdomen by Dr Osamah A. A. Alwalid
- CT ABDOMEN by Yuri
- Bt ilginc by Ayşe Rüksan Erdoğan
- Paeds Chest by Dr Scott Quadrelli
- abdomen by ahmed elfeky
- Congenital by Sohrab Towfighi
- Cardiac by Allister Howie
- congenital findings by Dr Leonard Tiong
- Paediatric Tony Chen by Dr Tony Chen
- Spleen by Dr Rusiru Gunawardena
- bizzare by Kholoud Morad
- chest by Dr Ali Basim
- GI by Taimur