Situs ambiguous (polysplenia syndrome type)

Case contributed by Dr MohammadTaghi Niknejad

Presentation

Heart murmur at physical exam

Patient Data

Age: 4
Gender: Male

The cardiac apex is on the right. Transverse liver is noted with stomach on the right and also multiple spleens on the right with interruption of intrahepatic IVC with azygous continuation of IVC.

Case Discussion

The findings are consistent with situs ambiguous (also called heterotaxy) - polysplenia syndrome type. 

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Case information

rID: 20894
Case created: 19th Dec 2012
Last edited: 7th Feb 2016
Inclusion in quiz mode: Included

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