Situs ambiguous (polysplenia syndrome type)

Case contributed by Dr Mohammad Taghi Niknejad

Presentation

Heart murmur at physical exam

Patient Data

Age: 4
Gender: Male

The cardiac apex is on the right. Transverse liver is noted with stomach on the right and also multiple spleens on the right with interruption of intrahepatic IVC with azygous continuation of IVC.

Case Discussion

The findings are consistent with situs ambiguous (also called heterotaxy) - polysplenia syndrome type. 

PlayAdd to Share

Case information

rID: 20894
Published: 19th Dec 2012
Last edited: 16th Jul 2018
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.