Situs ambiguous (polysplenia syndrome type)

Case contributed by Dr Mohammad Taghi Niknejad


Heart murmur at physical exam

Patient Data

Age: 4 years
Gender: Male

The cardiac apex is on the right. Transverse liver is noted with stomach on the right and also multiple spleens on the right with interruption of intrahepatic IVC with azygous continuation of IVC.

Case Discussion

The findings are consistent with situs ambiguous (also called heterotaxy) - polysplenia syndrome type. 

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Case information

rID: 20894
Published: 19th Dec 2012
Last edited: 21st Sep 2020
Inclusion in quiz mode: Included

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