Presentation
Heart murmur at physical exam
Patient Data
Age: 4 years
Gender: Male
From the case:
Situs ambiguous - polysplenia syndrome type
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The cardiac apex is on the right. Transverse liver is noted with stomach on the right and also multiple spleens on the right with interruption of intrahepatic IVC with azygous continuation of IVC.
Case Discussion
The findings are consistent with situs ambiguous (also called heterotaxy) - polysplenia syndrome type.