Solid pseudopapillary tumour of the pancreas

Case contributed by Dr Ian Bickle

Presentation

Teenage female with abdominal pain and a palpable mass in the upper abdomen.

Patient Data

Age: 15
Gender: Female

Large heterogenous mass in the epigastrium extending into the right upper quadrant.

Non hepatic derived.

Huge heterogenous mass arising from the head of pancreas with cystic elements compressing the IVC.

Double duct sign evident - dilated CBD and pancreatic duct.

 

Huge mass arising from the head of pancreas without internal diffusion restriction.

Double duct sign evident - dilated CBD and pancreatic duct.  Mild intrahepatic duct dilatation.

FNAC sample

Giemsa Stain: Cellular specimen showing solid and papillary fragments with myxoid stromal cores, and bland round-oval epithelial nuclei.

The pancreatic mass was resected en bloc with a segment of adherant transverse colon ( stitch ).

Case Discussion

Solid pseudopapillary tumour of the pancreas ( Franz ) tumour is a rare pancreatic mass almost exclusively in females typically in the 2-3rd decades of life.

The mass is typically large at presentation, well encapsulated and has both solid and cystic elements.   Ductal obstruction is infrequently identified.

The histological appearances are characteristic and from which the tumour derives its name.

PlayAdd to Share

Case information

rID: 34549
Case created: 25th Feb 2015
Last edited: 2nd Nov 2016
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.