Presentation
Facial asymmetry and left eye proptosis.
Patient Data
Age: 8 years
Gender: Female
From the case:
Sphenoid wing dysplasia
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Axial T2

Absence of the left sphenoid wing and the lateral orbital wall. Consequently the left temporal lobe with the surrounding CSF and enlarged arachnoid space are prolapsing into the left orbit producing distorsion of the left optic nerve and subsequent left proptosis.
From the case:
Sphenoid wing dysplasia
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Axial C+ portal venous phase

A gaping bony defect is seen in the posterior aspect of the left orbit giving the "empty orbit sign"
Absent anatomical landmarks of the optic nerve canal,anterior clinoid, superior and inferior orbital fissures.
Absent soft tissue masses.