Sprengel deformity

Case contributed by Dr Dalia Ibrahim

Presentation

Left shoulder deformity since birth

Patient Data

Age: 12 years
Gender: Female
X-ray

Elevated left scapula.

CT

Elevated left scapula.

An omovertebral bar (Osseus connection between scapula and cervical spine) is seen.

Hypoplasia/atrophy of the left shoulder girdle muscles.

CT

Elevated left scapula.

An omovertebral bar (Osseus connection between scapula and cervical spine) is seen.

Case Discussion

Sprengel deformity, or congenital elevation of scapula, is a complex deformity of the shoulder and is the most common congenital shoulder abnormality.

Sprengel deformity usually coexists with other congenital abnormalities, particularly those involving the vertebrae and ribs. An omovertebral bar (fibrous, cartilaginous and/ or osseus connection between scapula and cervical spine) is often present.

It is also commonly associated with hypoplasia or atrophy of regional muscles, and these associated features can cause further misshaping of the shoulder and limitation of shoulder movement.

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Case information

rID: 29259
Case created: 12th May 2014
Last edited: 14th Mar 2016
Inclusion in quiz mode: Included

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