Sturge-Weber syndrome

Case contributed by Ian Bickle
Diagnosis certain

Presentation

Female in 30's presents to A and E following a seizure.

Patient Data

Age: 30 years
ct

Gyriform calcification in the high left frontal lobe, with the characteristic 'tram-track' calcification.

Associated parenchyma volume loss.

Disproportionately large left frontal sinus compared to the right.

Choriod plexus symmeterical.

Case Discussion

Sturge Weber syndrome is one form of phakamatosis, characterized by a pial hemangioma in the brain with an associated facial hemangioma.

The leptomeningeal hemangioma results in a vascular steal affecting the subjacent cortex and white matter producing localized ischemia, hence the associated parenchymal volume loss.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.