Sturge-Weber syndrome

Case contributed by Dr Ian Bickle

Presentation

Female in 30's presents to A and E following a seizure.

Patient Data

Age: 30 years
CT

Gyriform calcification in the high left frontal lobe, with the characteristic 'tram-track' calcification.

Associated parenchyma volume loss.

Disproportionately large left frontal sinus compared to the right.

Choriod plexus symmeterical.

Case Discussion

Sturge Weber syndrome is one form of phakamatosis, characterized by a pial hemangioma in the brain with an associated facial hemangioma.

The leptomeningeal hemangioma results in a vascular steal affecting the subjacent cortex and white matter producing localized ischemia, hence the associated parenchymal volume loss.

PlayAdd to Share

Case information

rID: 26281
Published: 11th Dec 2013
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.