Sturge-Weber syndrome

Case contributed by Dr Utkarsh Kabra

Presentation

Seizures

Patient Data

Age: 5 years
Gender: Male
MRI

Gyriform calcifications in right frontal and parietal lobes appearing hypointense on GRE images.
Prominent vascular channels are seen in the right frontal lobe parenchyma and convexity sulci, likely draining into the anterior aspects of superior sagittal sinus.
Prominent vascular channels are also seen in the right sylvian fissure, temporal lobe and right cerebellar hemisphere, likely draining into the deep venous system.
Prominence of right frontoparietal and temporal convexity sulci seen – cerebral atrophy.
Mild prominence of the right choroid plexus.
 

Case Discussion

Overall above findings are suggestive of Sturge-Weber syndrome with prominent
collateral vessels.

Patient had a facial nevus on the ipsilateral side as that of the parenchymal abnormality.

CT was done elsewhere (images not available) which showed gyriform calcifications in the areas mentioned above.

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