Sturge-Weber syndrome

Case contributed by Dr Mahesh Gautam

Presentation

Recurrent seizures with port wine stain in the left side of face since birth

Patient Data

Age: 2 years
Gender: Male
CT

CT brain demonstrates gyral calcification in the left parietal, temporal and occipital lobes with parenchymal volume loss. 

MRI

Abnormal low signal on T1WI and  T2WI in the subcortical region of the left parietal lobe with associated volume loss. The corresponding region shows blooming on SWI. Prominent leptomeningeal vessels are in the left parietotemporal region with enlarged ipsilateral choroid plexus. Leptomeningeal enhancement is seen in the left parietotemporal region.

Case Discussion

Findings are typical of Sturge-Weber syndrome.

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