Presentation
Seizure and right-sided body weakness.
Patient Data
Age: 40 years
Gender: Female
From the case:
Sturge-Weber syndrome
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- abnormal low T2 signal at the subcortical white matter on the left side
- prominent abnormal vascular channels traversing the white matter of the left hemisphere, along with abnormally enlarged signal void deep venous drainage
- mild volume loss of the left cerebrum
- diffuse leptomeningeal enhancement of the left hemisphere
- disproportionately large left frontal sinus compared to the right
Case Discussion
Findings are consistent with Sturge-Weber syndrome which is a rare congenital vascular disorder that leads to progressive unilateral brain ischemia and subsequent atrophy.