Supratentorial PNET

Case contributed by Dr Jeremy Jones

Presentation

First seizure with sunsetting. Increasing head circumference and delayed motor milestones.

Patient Data

Age: 16 months
Gender: Female
Modality: MRI

The obvious intracranial mass lesion is a mixed solid and cystic lesion that is centered around the midline in the anterior cranial fossa. The more solid elements enhance and demonstrate diffusion restriction.

Features here are of a high-grade, aggressive tumour which is highly vascular. The differential includes supratentorial PNET and supratentorial ependymoma. The MRS is not particularly helpful.

Case Discussion

A biopsy of the central solid components was undertaken and revealed that the tumour was a supratentorial PNET. The biopsy of the lesion resulted in significant haemorrhage and 4 units of blood along with clotting factors were required.

Chemotherapy did not significantly alter the volume of MRI characteristics of the lesion and it continued to grow.

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Case Information

rID: 32198
Case created: 18th Nov 2014
Last edited: 6th Aug 2016
System: Paediatrics
Inclusion in quiz mode: Included

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