Total anomalous pulmonary venous return (TAPVR)

Case contributed by Aditya Shetty


Cyanosis; dyspnea.

Patient Data

Age: Neonate
Gender: Male

X-ray shows abnormal soft tissue shadows in bilateral para-tracheal areas. Bilateral lungs are clear.

Case Discussion

Case of total anomalous pulmonary venous return (TAPVR); a congenital cyanotic heart disease

The entire pulmonary venous flow is directed to the right atrium via SVC (i.e. all pulmonary veins to common pulmonary vein to vertical vein to innominate vein to SVC)

Right to left shunt (ASD) is present which is responsible for the cyanosis

The paratracheal shadow on the right is the prominent SVC and on the left is the vertical vein.

These prominent vessels along with the heart give a characteristic 'snowman' appearance; also referred to as 'figure of 8' sign. It is characteristic of TAPVR type I (supracardiac type)

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