Tuberous sclerosis - multiple angiomyolipomas

Case contributed by A.Prof Frank Gaillard

Presentation

Seizures and mental retardation

Patient Data

Age: 30
Gender: Female
Modality: CT

Both kidneys contain innumerable predominently fat density nodules. 

Modality: CT

Pre and post contrast CT scans through the brain demonstrate numerous calcified subependymal nodules. Heterogeneity of the sub-cortical white matter is also typical of hamartomas. 

Case Discussion

Tuberous sclerosis with multiple angiomyolipomas is a relatively common occurence. About 55-75% of TS cases are associated with angiomyolipomas.

This is a classical case demonstrating subependymal hamartomas and subcortical tubers, in case of multiple angiomyolipomas. 

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Case Information

rID: 8772
Case created: 1st Mar 2010
Last edited: 24th Nov 2015
Tags: kidneys, kidney, aml, ts
Inclusion in quiz mode: Included

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