Presentation
6-month progressive swelling, mildly bluish discoloration and warmth of the left shoulder. No functional impairment. Normal platelets and coagulation profile.
Patient Data
Ill-defined high T2WI signal and enhancement in the left shoulder region involving the subcutaneous fat, deltoid and supraspinatus muscles, intermuscular fasciae, scapula and axillary region.
Ill-defined stranding of subcutaneous fat in the left shoulder region with echogenic areas of fat and muscle. Minimally increased Doppler flow.
Case Discussion
The patient was seen in our vascular anomalies reference center.
Percutaneous biopsy revealed a tufted angioma. Along with kaposiform hemangioendothelioma, this is one of the two vascular tumors associated with the Kasabach-Merritt phenomenon (which was absent in this patient) according to the International Society for the Study of Vascular Anomalies (ISSVA) classification.