Undifferentiated embryonal sarcoma of the liver

Case contributed by Sam Digby

Presentation

Two week history of fevers and right upper quadrant pain.

Patient Data

Age: 30 years
Gender: Male

Large low density liver mass with enhancing septations.

A large heterogeneous lesion is noted in the right lobe of the liver. This is hyperechoic relative to the background liver, was thought to perhaps contain cystic spaces.

A large hepatic lesion is again noted, with heterogeneous high T2 signal intensity relative to the background liver. The lesion contains multiple low T2 signal bands, likely fibrous septae.

Heterogeneous high T1 internal signal is present in the lesion pre-contrast, suggestive of hemorrhage. Minor peripheral gadolinium contrast-enhancement is present.

Nuclear medicine

There is abnormal FDG avidity around the periphery of the large low density lesion in the right lobe of liver. Based solely on FDG PET, a distinction between a large liver abscess and a predominantly necrotic primary or secondary liver tumor cannot be made.

Histology Report

Embryonal sarcoma, with evidence of lymphovascular invasion.

Case Discussion

The patient proceeded to a partial hepatectomy, partial adrenalectomy and resection of the diaphragm. A biopsy was not performed.

Hepatic embryonal sarcoma is a rare tumor in the adult population.

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Case information

rID: 82820
Published: 17th Oct 2020
Last edited: 18th Oct 2020
Inclusion in quiz mode: Included
Institution: Austin Health

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