Presentation
Dyspnea
Patient Data
CT of the chest shows hypogenetic right lung, right sided tracheal deviation with absent right pulmonary artery. Contrast CT shows aberrant supply of the right lung from the celiac trunk which shows aneurysmal segment. Left lung shows anomalous pulmonary vessels.
Coronal projection shows cervico-dorsal scoliosis.
Case Discussion
Unilateral absence of the pulmonary artery is a rare congenital condition. It can occur as an isolated anomaly or in association with other congenital anomalies like TOF or aortic coarctation.
Clinically, patients may present with recurrent chest infection or with features of pulmonary hypertension.
In this case, the left pulmonary veins are dilated probably because the right heart output is directed only to the left lung.
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