Usual interstitial pneumonia - scleroderma related

Case contributed by Dr Bruno Di Muzio


Clinically established scleroderma. Shortness of breath.

Patient Data

Age: 74-year-old
Gender: Female

Diffuse reticular changes bilaterally are similar and compatible with fibrosis in the setting of scleroderma.

No superimposed consolidation is appreciated.

The cardiomediastinal contours are normal.

The bones are diffusely osteopaenic and there appears to be at least one mid-thoracic vertebral crush fracture.

CT chest demonstrating peripheral apicobasal interstitial involvement characterized by reticular opacities associated with micro and macro honeycombing foci and some traction bronchiectasis. Ground-glass opacities are not a prominent feature in this study. Lung volumes are overall preserved. No evidence of esophageal dilation. 

Case Discussion

This case illustrates imaging follow-up in a patient with a known diagnosis of scleroderma and demonstrating scleroderma-related interstitial lung disease, which has a usual interstitial pneumonia (UIP) pattern. 

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Case information

rID: 45314
Published: 25th May 2016
Last edited: 26th May 2016
System: Chest
Tag: rmh
Inclusion in quiz mode: Included

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