Vertical fusion defects of the mullerian duct (septate uterus and transverse vaginal septum)

Case contributed by Dr Amr Farouk

Presentation

25 days female neonate presented with abdominal distention & vulval mass.

Patient Data

Age: 25 days
  • The pelvis & lower abdomen center are seen occupied by bi-compartmental  longitudinally positioned thick walled cystic structure with thick mid-line wall. It measured 3X5.4X5.6 cm along its maximal axial & craniocaudal dimensions.The cavities are seen distended with fluid density reading a mean attenuation 3-5 HU. The urinary bladder is seen compressed opposite anterior abdominal wall.
  • A cystic lesion is seen sagging from the introitus with area of collasped wall seen at the level of presumed vagina being continuous superiorly with the thick mid line wall of the fore-mentioned lesion. It measured 3.3X4.5 cm along its maximal axial & craniocaudal dimensions.
  • The left kidney shows an oval shaped thick wall cyst at its mid-zone posteriorly showing high density fluid reading a mean attenuation 15 HU & measuring 1.8X1.4 cm in diameters.

Case Discussion

Combined manifestation of vertical fusion defects of the Mullerian duct in the form of septate uterus and transverse vaginal septum causing massive retained secretions & bulging vaginal septum. 

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Case information

rID: 38897
Case created: 10th Aug 2015
Last edited: 28th Oct 2017
Inclusion in quiz mode: Included

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