von Hippel Lindau

Case contributed by Assoc Prof Frank Gaillard

Selected MRI images demonstrate multiple enhancing intramedullary lesions, the largest at C4/5, with an associated syrinx. 

DSA (angiography)

Catheter angiography demonstrates the cord lesions to be very hypervascular consistent with hemangioblastoma. 


MRI demonstrates a left inferior pole renal mass consistent with a renal cell carcinoma. 

Case Discussion

This individual has established von Hippel Lindau disease with a renal cell cancer on the left and cervical cord hemangioblastomas with an associated syrinx.

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Case information

rID: 8348
Published: 24th Jan 2010
Last edited: 24th Feb 2020
Inclusion in quiz mode: Included