Presentation
Previous history of posterior fossa operation. Presented with recurrent headache.
Patient Data
Two space-occupying lesions are seen at the bilateral cerebellar hemispheres located at the anteroinferior aspect of the left cerebellar hemisphere and at the posterolateral aspect of the right cerebellar hemisphere. Both lesions show small cystic components and avidly enhancing solid nodules.
No other enhancing lesions however there are areas of gliosis and encephalomalacia at both cerebellar hemispheres more evident on the right side (sequalae of previous operation).
The patient went on to have a resection.
Pathology report
Nature of the specimen: cerebellar mass, partially solid and partially cystic.
Gross description: small pieces of tissue, totalling 2.0 x 1.5 x 1.0 cm.
Microscopic examination:
This is a tumor consisting of numerous capillary and venous-type vessels with cells with vacuolated-cleared and eosinophilic cytoplasm in between.
Final diagnosis: hemangioblastoma (WHO grade I).
Multiple small cysts are seen within the pancreas and both kidneys.
Small avidly enhanced nodule is seen within the right suprarenal gland measuring 1.5cm most likely representing pheochromocytoma.
Case Discussion
Multiple hemangioblastomas, renal cysts, pancreatic cysts and adrenal pheochromocytoma all are features of von Hippel-Lindau syndrome.
Unable to process the form. Check for errors and try again.