Von Hippel-Lindau disease - pancreatic manifestations

Case contributed by Ali Hekmatnia
Diagnosis almost certain

Presentation

Von Hippel-Lindau disease and symptoms of pancreatic exocrine insufficiency.

Patient Data

Age: 35 years
Gender: Female

The pancreatic parenchyma is replaced by multiple innumerable pancreatic cysts. Cystic lesions do not communicate with the main pancreatic duct.

Case Discussion

MRI and MRCP of the pancreas of a patient with Von Hippel-Lindau disease demonstrating innumerable pancreatic cysts.

Case courtesy of Dr Fateme Hosseinabadi.

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